Non compaction kardiomyopathie. Dilated cardiomyopathies and non

, Schneider J Eur Heart J 32:1446—1456• Eur Heart J
Yelbuz, B , Habib G
The low number of reported cases though is due to the lack of any large population studies into the disease and have been based primarily upon patients suffering from advanced heart failure Patient prognosis is determined by the occurrence of heart failure and arrhythmias
Am J Cardiol 108:1021—1023• Noncompaction cardiomyopathy NCCM is a genetic myocardial disorder, which is characterized by a two-layered ventricle wall with a thin compact outer layer and a noncompacted inner layer, with prominent trabeculations and deep intratrabecular recesses communicating with the ventricle cavity without any contact to the coronary system Weiford, V
1996;93 5 :841—842
Keywords: Arrhythmias, cardiac; Genetics; Heart failure; Myocarditis; Peripartum cardiomyopathy Likewise it possible to have severe heart failure, which even though the condition is present from birth, may only manifest itself later in life
, Robson M Petersen S
; Tokala, Hemasri; Gosavi, Aparna; Gupta, Vishal 2010-01-01 Es konnten verschiedene Mutationen des Gens , ein Enzym des -Stoffwechsels, nachgewiesen werden
Major clinical correlates include systolic and diastolic dysfunction, associated at times with systemic embolic events Genetic related• Eur Heart J 29:270—276• Owing to the growing possibilities of genetic diagnostics, increasingly more triggering variants and hereditary mechanisms emerge

Ichida F, Hamamichi Y, Miyawaki T et al 1999 Clinical features of isolated noncompaction of the ventricular myocardium: long-term clinical course, hemodynamic properties, and genetic background.

Retrieved June 15, 2007.

Curr Opin Pediatr 19:619—627• Much attention must be paid in order to:• Murphy RT, Thaman R, Blanes JG et al 2005 Natural history and familial characteristics of isolated left ventricular non-compaction.

Kobza R, Steffel J, Erne P et al 2010 Implantable cardioverter-defibrillator and cardiac resynchronization therapy in patients with left ventricular noncompaction.

, Vidal V.

, Abbara S.

As normal development progresses, these trabeculated structures undergo significant compaction that transforms them from spongy to solid.

A publication is expected by Leiden University Medical Centre• 6 described the criteria for the diagnosis by CMR: the ratio of noncompacted myocardium to compacted myocardium must be greater than 2.

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